Otosclerosis
Introduction
Aetiology
Pathology
Clinical Picture
Examination
Audiological Tests
Differential Diagnosis
Treatment
Otosclerosis
Oto,
sclerosis
Mature lamellar bone is replaced by
unorganized spongy bone of greater
thickness and vascularity
Common
disease, 1: 200
Frequently in fair females
Progressive hearing loss
Familial tendency
Aetiology
Unknown aetiology
Disorder affecting growth of collagen
Many theories:
Genetic
Race
Sex
Age of onset
Pregnancy
Infection
Immune disorder
Trauma
Metabolic
Vascular
Anat./Histological abn of temporal bone
Pathology
Hereditary disease
Disease of otic capsule
Phases of bone resorption & bone
formation
Removal of mature bone by osteoclasts
Replacement by woven bone of more
cellularity, vascularity and thickness
SITES
Any part of temporal
bone
Fistula ante fenestrum
Fistula Post fenestrum
Oval window
Round window
Promontory
Cochlea
B/L sym. Affection
Physiologic Effect
Before
After
Symptoms
Deafness
Tinnitus
Paracusis willisi
Family history
Low modulated voice
Vertigo
Examination
External Ear Examination - Normal
Tympanic Membrane normal
Flemingo pink blush
Eustachian Tube patent
Blue sclera & fragile bone as part of Vonder Hoeve syndrome
Tuning Fork test
Rinnes
Weber
ABC
test
test
Negative
Lateralized to deafer
ear
Normal
Audiological test
Pure
tone audiometery
Conductive
Mixed
loss dip at 2K
loss
Sensory loss
Conductive Deafness
Mixed Deafness
Sensori-neural Deafness
Impedance Audiometry
Helps
to diff. from other causes of
conductive loss
Type As curve
Type B curve in SOM
Type C In E. T. catarrh
Type Ad in Ossicular discontinuity
Normal Impedance
Ossicular Discontinuity
As Curve
Differential Diagnosis
Otitis media with effusion
Ossicular discontinuity
Adhesive ottitis media
Cong. Footplate fixation
Tympanosclerosis
Cong. Cholesteatoma
CSOM
Vender Hoeve syndrome
Treatment
Medical
treatment
Surgical treatment
Hearing rehabilitation
Medical Treatment
Sodium flouride
50mg-75
Decreases
mg daily x 2 yrs
osteoclastic activity
Increases osteoblastic bone formation
Indications
Positive Schwartz sign
Progressive SN loss with surgically confirmed otosclerosis
SN loss with positive family history
Positive Radiological Evidence
Contra indication
Chronic Nephritis
Rheumatoid arthritis
Pregnant & lactating mother
Age < 18 yrs
Allergy to Sod. Fluoride
Skeltal flourosis
Peptic ulcer
Surgical Treatment
Fenestration
Stapes
mobilisation
Stapedectomy
Stapedotomy
Criteria for Stapedectomy
Conductive loss not < 30db
Good cochlear reserve
Good speech discrimination
Conductive loss not > 60 db
Indications for Stapedectomy
Otosclerosis
Tympanosclerosis
Pagets disease
Congenital foot plate fixation
Contra indications
Active
disease
Pregnancy
Poor cochlear reserve
Only hearing ear
General medical disease
Vertigo
Procedure
Local
Infiltration
INCISION
Flap elevation
Lifting Annulus
Exposure of Stapes
Stapedial Tenotomy
Supra structure Removal
Piston in Place
Stapedotomy
Sound Conduction After Surgery
Post op Advise
Not to blow nose forcefully
Not to sneeze with closed mouth
Avoid loud noises
Not to climb mountains, Not to board non
pressurized aircraft.
Report to Surgeon for Vertigo/Decreased
hearing
Diving when swimming
Lifting heavy weights
Hearing rehabilitation
Hearing Aids
Pocket
BTE
ITC
Model