Cerebral palsy
By Andaleeb zehra
Definition
[Link] little who first defined
cerebral palsy, described the condition
as “ a persistent disorder of movement
and posture appearing early in life and
due to a developmental non-
progressive disorder of the brain.”
[Link] Bobath elaborates that “ the
lesion affects the immature brain and
interferes with the maturation of the
central nervous system, which has
specific consequences in terms of the
type of cerebral palsy which develops,
its diagnosis, assessment and
treatment.
Prevalence rate
A reasonable estimate of the
prevalence of cerebral palsy is 2 per
1000 live births (Paneth et al,1981).
Cerebral palsy is the most common
motor disorder in children occurring
in 2-2.5 per 1,000 live births (Stanley
et al,2000)
Causes of cerebral palsy
Pre natal causes
Peri natal causes
Post natal causes
Pre-natal causes
Trauma during pregnancy
Infection like jaundice or any other infection
to the mother during gestation.
Any drug disorder
Pre eclampsia, eclampsia
Any genetic cause
Any condition due to vascular change
Asphyxia
Defective development of the foetus
Peri–natal causes
The birth asphyxia – knotted umbilical cord
around the foetus or umbilical cord
strangulated around the foetal head.
Forceps delivery
Breech delivery – especially occurring
through a partially dilated cervix, and
without forceps applied to protect the head.
Premature baby
Birth anoxia
Post-natal causes
Delayed birth cry leads to hypoxia
Severe infection like rubella and
cytomegalovirus, neonatal encephalitis
and meningitis.
Hypoglycemia
Severe jaundice
There could be occlusion of MCA or
internal carotid artery
Classification of topography
Quadriplegia – involvement of all four
limbs
Diplegia – involvement of 4 limbs with
legs more affected than arms.
Paraplegia – both lower limbs are
affected
Hemiplegia – one side of the body is
affected
Monoplegia – one limb is affected.
Perlstein 1949, 1952
Degree of Severity
◦ 1. Mild CP
◦ 2. Moderate CP
◦ 3. Severe CP
Types of cerebral palsy
Spastic
Athetoid
Ataxic
Flaccid
Mixed
Spastic cerebral palsy
It is caused by the damage to the upper
motor neuron in the cerebral cortex or along
the pathways which terminate in the spinal
cord.
There is hypertonous or clasp knife variety.
If these spastic muscles are stretched at a
speed they respond in an exaggerated
fashion, they contract blocking a movement.
This hyperactive stretch reflex occur at the
beginning, middle or near the end ROM.
There are increased tendon jerks, occasional
clonus and other signs of UMN lesions.
Abnormal postures :
these are usually associated with the
antigravity muscles. The abnormal postures
appear as unfixed deformities which may
become fixed deformity or contractures.
Voluntary movements: spasticity doesn’t
mean paralysis. Voluntary motion is present
but may be laboured, there maybe weakness
on initiation of movement or movement at
different part of its range.
If spasticity is decreased or removed by
treatment or drugs, the spastic muscles
maybe found to be more weak or more
strong.
Once the spasticity decreased the
antagonist muscle may also be stronger
once they no longer have to overcome the
resistance of tight spastic muscles
However in time these antagonist may have
to become weak with disuse atrophy.
Voluntary movements are present but they
are clumsy and uncoordinated.
Intelligence – it varies but may be more
impaired than in children with athetoid
cerebral palsy.
Perceptual problems – specially of spatial
relationships are more common in spastic
type of cerebral palsy.
Sensory loss occasionally occurs with the
child with [Link] maybe visual
field loss and lack of sensation in hand.
Growth of the hemiplegic limb can be less
than on the unaffected side.
Rib cage abnormality and poor respiration
may exist.
Epilepsies are more common in this case as
compared to other types of cerebral palsies.
Athetoid
Athetosis: these are bizarre purposeless
movements which may be uncontrollable. The
involuntary movement maybe slow or fast.
They maybe jerky, tremor, swiping or rotary
patterns or they maybe unpatterned. They are
present at rest in some children.
the involuntary movement is increased by
excitement, any form of insecurity and effort
to make a voluntary movement.
Factors which decrease athetosis are:
Fatigue
Drowsiness
Fever
Lying prone
Child’s attention deeply held
Athetosis maybe present in all parts of the
body including face and tongue. The
athetosis may sometimes only appear in
hands and feet or in the proximal joints or in
both proximal or distal joints.
Postural control:
The involuntary movement of dystonic spasm
may throw a child off balance. However, the
well known instability in athetoids is often
indirectly connected with postural
mechanism.
Voluntary movement
these are possible but there may be an initial
delay before the movement is begun.
The involuntary movement may partially or
totally disrupt the willed movement making it
uncoordinated
There is lack of fine motor movements.
Hypertonia or hypotonia
Either may exist or there maybe fluctuations of
tone.
Athetoids are sometimes called as tension or non
tension types.
There maybe dystonia or twisting of head , trunk or
limbs.
Sudden spasm of flexion or extension could occur.
The hypertonia is rigidity but occasionally spasticity
may be present specially in athetoids quadriplegics.
The fluctuating tone sometimes occur with
fluctuation of mood or emotions.
Paralysis of gaze muscles
May occur so that athetoids may find it
difficult to look upwards and sometimes also
to close their eyes voluntarily.
Athetoid dance
Some athetoids are unable to maintain weight on
their feet and continually withdraw their feet
upwards or upwards and outwards in an athetoid
dance.
They may take weight on one feet while pouring
or scrapping the ground in withdrawal motion
with the other leg.
This has been attributed to a conflict between
reflexes specially grasp and withdrawal reflexes.
The conflict of reflexes may also be seen in the
hand.
Intelligence is frequently good and may be
very high. Occasionally intellectual
impairments may also be present.
Hearing loss is specific high frequency type.
‘drive’ and outgoing personalities are often
observed among the athetoids.
Emotional liability is more frequent than in
other cerebral palsies.
Articulatory speech difficulties and
breathing problems may be present.
Ataxic
Disturbance of balance:
There is poor fixation of head, trunk,
shoulder and pelvic girdle.
Some ataxic overcompensate for this
instability by having excessive balance saving
reactions in arms
Instability is also found in athetoids and
spastics.
Voluntary movements
Present but clumsy or uncoordinated.
The child over reaches or under reaches for
an object and is said to have dysmetria.
Now this inaccurate limb movement in
relation to its objective may also be
accompanied by intention tremors.
The fine movement of the hand maybe
poor.
Hypertonia:Hypertonia is usual. Ataxia may
be present in hypertonic cases as well.
Nystagmus may exist.
Intelligence impairments appear especially in
presence of visual and perceptual problems.
Clumsy, intelligent children are sometimes
diagnosed as ataxic cerebral palsy.
A pure ataxic is rarely diagnosed.
Physiotherapeutic management
The treatment should be aimed at the
neurological mechanism of posture, balance,
movement supplemented by procedures for
muscles and joints when necessary. This needs
to be integrated into motor learning models.
There should not be rigid adherence to
particular diagnostic classification in treatment
programmes.
Aetiology may not influence the treatment in
cerebral palsy
Emphasis should be given to train various
postural mechanism which are absent or
abnormal in all types of cerebral palsy or may
be absent in any developmental motor delay.
Treatment should provide features if motor
disorders such as hypotonicity, hypertonicity,
involuntary movement, weakness, abnormal
pattern of voluntary movement, abnormal
reflex in context of total motor function as
well as the specific treatment for individual
cases.
Therapist should deal with abnormal reflexes
only in those cases where they directly
disrupt function.
The therapist must deal with the complex
situation of pathological symptoms which in
the context of a developing child in the
cerebral palsy and other motor disorders.
The developmental schedule or sequence of
normal child should only be used as a
guideline and adaptations should be
according to each child.
The treatment should commence as early as
possible in order to get good results.
The treatment plan should be reviewed
periodically to take account of changes in the
clinical picture as a child grows older.
Physiotherapist needs to include learning
principles in their work which also include
emotional issues.
techniques
The handling techniques aims to
promoting :-
Child assests and ability and if possible to
stimulate normal pattern of movement.
To reduce or prevent deformity
To discourage position, movement and
behaviour that makes handling difficult
To develop independence in daily activities
To promote child ability and stimulate normal
pattern of movement.
To play and develop recreational activity
To decrease spasticity
Improve muscle power and range of motion of joints
Improve static and dynamic balance
Improve gait and walking pattern
Improve functional deformity
To develop some form of mobility which may include
wheelchair, walker and electronic mobile wheelchair.
Treatment should be aimed at neurological
mechanism of posture, balance and movement.
Treatment should be aimed for motor disorders such
as hypertonicity,hypotonicity, involuntary movement,
weakness, abnormal pattern of voluntary movement.
Techniques included are:
Lifting and carrying
Positioning
Position for function
Movement between position
Mobilization activity
Passive stretching
Hydrotherapy
PNF techniques
Muscle power and strengthening
Occupational and speech therapy
Walking aids
Lifting and carrying techniques
The child should be lifted keeping a straight
back with a wide base of support, knees
bended, holding the child as whole as
possible.
For flex children constant extend positioning
should be favoured for extending or thrusting
positioned child.
The adult’s hand may be under or in front of
the child’s knee in either method of carrying
or lifting.
positioning
Lying supine:
Many cerebral palsy patient are completely
unable to function and in this position they
are most asymmetrical.
If this position has to be used, a pillow
should be placed under head and shoulders.
Side lying
It’s a position in which child could be very
asymmetrical. Both the hands are in his range
of vision and are more likely to be used
together.
Care must be taken that the child doesn’t fall
partially into prone or supine lying.
sitting
Long sitting with knees slightly flexed or straight
is the position in which normal baby learns to
establish his bottom and legs as his base of
support.
Sitting is a posture in which the hamstrings and
the hip adductors can be stretched.
The child is unable to sit flat on the floor without
this pelvis rotating posteriorly.
In such a case he can be placed so that his
bottom is slightly raised. Such as on a very low
stool or on a pile of books.
standing
The cerebral palsy child who in not able to
stand on his own by the age of 12-18 months
should be able to stand with the help of
therapist or the attendants.
Hips should be extended, slightly externally
rotated and abducted.
The knees should be straight.
The feet should be plantigrade.
Positioning for function
Improve exhalation and breath control for
speech can often be obtained in prone lying
or standing.
Balance exercises
Head and neck control in prone lying
Trunk control in sitting
Standing balance by weight shifting
Adaptive device and orthotic may be used as
HKAFO, KAFO, AFO, cervial collar, walking
aids etc.
Muscle strengthening
By hydrotherapy
Whirlpool bath
Suspension therapy
Active free exercise (with some resistance)
Physio ball can also be used.
Passive stretching
Hip adductors, quadriceps, hamstrings,
tendoachilles, calf muscles, biceps, triceps,
abductors and adductors of shoulders
Neck extensors
15 modules
Specific combination of these modules is used
for specific type of cerebral palsy
Module 1 : massage for hypotonic muscle but
this is contraindicated in spastic and athetoid.
Module 2 : passive motion through joint range
for mobilising the joints
Module 3 : Active assisted movements
Module 4 : Active motion
Module 5 :resisted motion is followed
according to child’s ability
Module 6 : conditioned motion is
recommended for babies, young children and
children with certain degrees of MR.
Module 7 : confused motion which involves
resistance to a muscle group in order to
contract an inactive muscle. Mass movements
such as extensive thrust or the flexion
withdrawal reflex are usually used.
Module 8: combined motion is the training
motion of more than one joint such as
shoulder and elbow flexion using the
modules 2,3,4 and 5.
Module 9 :relaxation techniques are those of
conscious letting go of the body and its
parts. these methods are usually used with
the athetoid type of cerebral palsy.
Module 10: movement from relaxation is
conscious control of movements, once
relaxation has been achieved. It is mainly
used in children to control involuntary
movements.
Module 11 :rest periods of rest are suggested
for all types of cerebral palsies.
Module 12: reciprocation : it is the training
movement of one leg after another in a
bicycling pattern
Module 13 : balance : the balance is aimed to
be achieved in all positions possible. For eg
training of sitting balance, training to stand
with the help of braces.
Module 14 : reach grasp and release is used for
training of hand function
Module 15 : skills of daily living such as
feeding, dressing washing and toileting are
mastered. Many aids can also be achieved for
achieving independence in ADL’s.